ANAESTHETIC MANAGEMENT OF A PATIENT WITH XERODERMA PIGMENTOSA OPERATED FOR BASAL CELL CARCINOMA OF SCALP
Journal Title: Journal of Evolution of Medical and Dental Sciences - Year 2018, Vol 7, Issue 11
Abstract
PRESENTATION OF CASE Xeroderma pigmentosa[1] is an Autosomal Recessive Genetic disorder of DNA repair, in which the activity to repair damage caused by UV light is deficient. Multiple BCC (Basal Cell Carcinoma) and other skin malignancies frequently occur at a young age in those with Xeroderma pigmentosa. It is a rare disorder characterised by hypersensitivity to sunlight; ocular involvement and progressive neurological complications. These manifestations[2] are due to UV radiations leading to a defect in repair of DNA by process of Nucleotide Excision Repair (NER). It leads to several challenges in Anaesthetic Management. Here, we are presenting the challenges in Anaesthetic Management in a case of 22 years old male patient suffering from Xeroderma pigmentosa posted for an oncosurgery (BCC of scalp).
Authors and Affiliations
Sushil Chand Verma, Ankesh Ankesh, Ajit Gupta
Keywords
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- EP ID EP411649
- DOI 10.14260/jemds/2018/324
- Views 81
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