Gorham's Syndrome Associated with Chiari I Malformation and Recurrent Meningitis without Fistula: Case Report
Journal Title: Journal of Clinical and Diagnostic Research - Year 2018, Vol 12, Issue 5
Abstract
ABSTRACT Gorham’s syndrome is a rare osteolytic disease in which progressive and spontaneous resorption of bone occurs. We present a case of a boy who presented with Chiari I malformation and recurrent meningitis without fistula. The patient was submitted to occipital bone biopsy and due to lymphocytic infiltration and intraosseous vascular ectasia the diagnosis of Gorham-Stout Syndrome was made. The patient underwent conservative treatment but, unfortunately he died by cardiorespiratory arrest secondary to atlanto-occipital dislocation. This case emphasizes the rarity of this pathology and the previously unreported association with recurrent meningitis without fistula.
Authors and Affiliations
Fernando Antônio Oliveira Costa, Othello Moreira Fabião Neto, Frederico Lima Gibbon, Guilherme Gago Silva, Luciana Azambuja Al Alam
Keywords
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- EP ID EP523194
- DOI 10.7860/JCDR/2018/35304.11565
- Views 75
- Downloads 0
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