Hernia in Mucopolysaccharidoses patients: a surgical challenge

Journal Title: Journal of Indira Gandhi Institute of Medical Sciences - Year 2017, Vol 3, Issue 2

Abstract

Abstract Mucopolysaccharidoses patients tend to have large hernia at multiple sites which are prone to recurrences due to tissue weakening. They are difficult cases for surgery and usually need some form of abdominal wall repair as herniotomy alone does not suffice. We present two such cases – one with Hunter syndrome and the other with Hurler syndrome to stress upon the salient clinical features and management.

Authors and Affiliations

Sandip Kumar Rahul, Ramdhani Yadav, Vijayendra Kumar, Vinit Kumar Thakur, Zaheer Hasan, Sweta Kumari

Keywords

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  • EP ID EP288691
  • DOI -
  • Views 61
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How To Cite

Sandip Kumar Rahul, Ramdhani Yadav, Vijayendra Kumar, Vinit Kumar Thakur, Zaheer Hasan, Sweta Kumari (2017). Hernia in Mucopolysaccharidoses patients: a surgical challenge. Journal of Indira Gandhi Institute of Medical Sciences, 3(2), 45-47. https://www.europub.co.uk/articles/-A-288691