Isolated and Recurrent Peripheral Facial Palsy Revealing Primary Sjogren’s Syndrome
Journal Title: Online Journal of Neurology and Brain Disorders - Year 2019, Vol 2, Issue 3
Abstract
Peripheral facial palsy (PFP) is often idiopathic; a secondary systemic cause is noted in less than 1.2% of cases. Primary Sjogren’s Syndrome (PSS) remains an exceptional and often insufficiently known etiology of facial paralysis, and only a few sporadic cases are reported in the medical literature. These inaugural forms of the disease represent a real diagnostic challenge for clinicians. We report an original observation of isolated and recurrent PFP as inaugural symptom of PSS in a 53-year-old female with no notable pathological history. Primary Sjögren’s syndrome (PSS) is an autoimmune disease characterized by focal lymphoid infiltration of the exocrine glands, mainly manifested by dry ocular and oral syndrome [1]. During the course of the disease, one-third of the patients develop extraglandular lesions: pulmonary, neurological, renal, hepatic and cardiac, which signal the systemic nature of this disease and condition its prognosis [2,3]. The prevalence of this connective tissue disease is estimated at 1-3% of the general population [1,4] and can reach as much as 4.8% in Europe [2]. The neurological manifestations of this disease are observed in 15-20% of cases and are highly polymorphic and far dominated by peripheral neuropathy [5-8].
Authors and Affiliations
Salem Bouomrani, Mouna Guermazi, Souad Yahyaoui, Nesrine Regaïeg, Hassène Baïli
Keywords
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- EP ID EP603494
- DOI 10.32474/OJNBD.2019.02.000137
- Views 74
- Downloads 0
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