Multifocal Dermatofibrosarcoma Protuberans
Journal Title: International Journal of Clinical & Experimental Otolaryngology (IJCEO) - Year 2016, Vol 2, Issue 1
Abstract
Background: Dermatofibrosarcoma Protuberans (DFSP) is an exceptionally rare soft tissue tumor that spreads locally with rare metastasis limited to brain, lung, and liver. Immunocompetent patients presenting with more than one DFSP are rare. Methods and Results: A 47 year old man presented with metachronous lesions of the left mastoid skin and right supraclavicular fossa skin. Biopsies revealed DFSP in both locations. CT scans never showed bony invasion in either location. Multiple excisions and radiation therapy have resulted in no recurrence at the supraclavicular site and recurrence in the mastoid site. Conclusions: DFSP can recur despite wide and deep excision combined with radiation therapy. The treatment algorithm for DFSP in the Head and Neck region is included in our review of the literature. Long term follow up is mandatory in these patients.
Authors and Affiliations
David Myssiorek
Keywords
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- EP ID EP206689
- DOI 10.19070/2572-732X-160003
- Views 120
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