Partial anomalous pulmonary venous connection (RCD code: II-3C.0)
Journal Title: Journal of Rare Cardiovascular Diseases - Year 2013, Vol 1, Issue 2
Abstract
A 48-year-old woman was admitted to our institution with a year’s history of uncharacteristic chest pain episodes and decrease in exercise tolerance. A CT lung scan performed nine months earlier revealed an anomalous vein arising from the right lower pulmonary lobe and draining into the inferior vena cava. A chest radiogram performed 2 months prior to the admission showed a curved shape adjacent to the right heart border. Right heart catheterization revealed: normal systolic, diastolic and mean pulmonary artery pressures, normal pulmonary resistance and insignificant shunt volume. Pulmonary artery angiography demonstrated an anastomotic vessel between the aberrant pulmonary vein and the right upper pulmonary vein. The patient was diagnosed with Partial Anomalous Pulmonary Venous Connection in form of Scimitar syndrome. Given a mild character of symptoms, no signs of the right-sided heart volume overload, insignificant shunt fraction and normal pulmonary circulation parameters, the patient was qualified to a conservative treatment with a close medical observation. JRCD2013; 1 (2): 39–41Key words: partial anomalous pulmonary venous connection, scimitar syndrome, left-to-right shunt, pulmonary hypertension
Authors and Affiliations
Leszek Wrotniak, Grzegorz Kopeć, Lidia Tomkiewicz-Pająk, Anna Kabłak-Ziembicka, Tadeusz Przewłocki, Piotr Podolec
Keywords
Related Articles
- EP ID EP245381
- DOI 10.20418/jrcd.vol1no2.81
- Views 106
- Downloads 0
Coronary fistula to the right atrium
We present the case of a patient with a large coronary fistula.Coronarography of the patient admitted to the Cardiology Department with STE‐ACS revealed a large fistula from the circumflex branch of the left coronary art...
Ophthalmic manifestations suggesting Kearns--Sayre Syndrome among young adults with cardiac conduction defects (RCD code: III-1A.5a)
Kearns-Sayre Syndrome is a multisystemic mitochondrial cytopathy characterized by specific ophthalmic signs, cardiac conduction disturbances with endocrine, musculoskeletal and central nervous system involvement. As a hi...
Prognostic value of inflammatory markers in acute coronary syndrome in a population with premature cardiovascular disease
Introduction: Inflammation plays a significant role in the development of atherosclerosis, and inflammatory markers could be used in risk assessment of patients with ischaemic heart disease. The use of such markers could...
An adult patient with tetralogy of Fallot and anomalous left anterior descending artery after conduit type of repair (RCD code: IV‑2A.1)
Tetralogy of Fallot is one of the most common cyanotic congenital cardiac disease concerning 10% newborn with congenital heart failures. About 3% of those patients have anomalous left anterior descending coronary artery....
4th Symposium on Rare Cardiovascular Diseases – ESC Barcelona 2014
Raport from the Satellite Symposium on Rare Cardiovascular Diseases.