Radio-diagnosis of Herlyn Werner Wunderlich Syndrome a rare case of urogenital abnormality
Journal Title: International Archives of Integrated Medicine - Year 2018, Vol 5, Issue 10
Abstract
Herlyn-Werner-Wunderlich syndrome (HWWS) is a very rare urogenital abnormality, which is characterized by Mullerian duct anomaly with associated mesonephric duct anomaly. This syndrome is also known as OHVIRA (Obstructed hemivagina with Ipsilateral Renal Anomaly). The incidence of Mullerian Duct Anomaly is 2-3%, and incidence of OHVIRA is 0.16 to 10% of that. The three important components of Herlyn-Werner-Wunderlich (HWW) syndrome are didelphys uterus, obstructed hemivagina and renal agenesis on the same side. Typically presents with pelvic pain in young females after menarche. Presentation in the reproductive age group is unusual. The most common renal anomaly associated with this condition is renal agenesis. Other renal anomalies include renal dysplasia, duplication of kidneys and ureters, crossed fused ectopia and ectopic ureter. Ultrasound and Magnetic resonance imaging are considered as the vital modalities for detection. MRI is the gold standard modality for assessing the anatomical characteristics of the uterus, cervix, and vagina. Early diagnosis helps to prevent complications such as endometriosis, pyocolpos, adhesions, infertility. The unique feature of our case is a presentation in the reproductive age group. Only very few case reports of OHVIRA with a presentation in the reproductive age group are available in the literature. Whenever there is a renal anomaly or renal agenesis, screening of pelvic organs is important in a female child for early detection of Mullerian duct anomalies and prevention of further complications.
Authors and Affiliations
Krithika S, Gurubharath I, Harshavardhan B, Dr. Baary
Study of expression of P53 in Gastric Carcinoma – As a prognostic indicator
Cancer of stomach remains the major cause of mortality worldwide despite a marked decline in the incidence of gastric carcinoma in the industrialized nations. Gastric cancer is the end result of multifactorial, multigene...
Study of PAP smear examination in patients complaining of leucorrhoea - A 2 years prospective study in a teaching hospital
Background: Leucorrhoea is the clinical evidence of infection and can be treated satisfactorily whenever diagnosed. Occurrence of cervical cancer associated with discharge/leucorrhoea can be easily prevented if detected...
A cross-sectional analytical study on the association of body mass index to dynamic lung volumes – assessed by digital spirometer in a tertiary care hospital in Chennai
Introduction: Obesity causes reduction of Lung compliance leading to decrease in lung volumes producing mostly a restrictive type of ventilatory defect. Compression of the thoracic cage by excessive fat and increased poo...
Intracranial ruptured dermoid cyst presenting as dysarthria: A case report
Intracranial dermoid cysts are tumors which are rare and are derived from ectopic epithelial cells. These dermoid cysts are slow-growing and are benign; they can cause morbidity by compressing the neurovascular structure...
Role of CT scan in diagnosis of HELLP syndrome: Radiologist’s perspective
Background: HELLP syndrome is life threatening condition. Diagnosis of HELLP syndrome plays an important role in assessment of complication. It can be done by USG and CT scan. Objectives: The aim of this study was to de...