Systemic Mastocytosis- A Case Report
Journal Title: International Journal of Biomedical Research - Year 2015, Vol 6, Issue 11
Abstract
Mastocytosis is a rare heterogenous disease characterized by the presence of excessive number of mast cells in various organs mainly in skin and bone marrow. .The incidence was 1 in 1,000 to 8,000 patients. It can follow a benign or indolent course, or it may be associated with life threatening symptoms. We report a rare case of 2 month old female child presented with hyperpigmented macular rash all over the body and few nodular lesions in popliteal and inguinal regions. The skin biopsy and bone marrow examination revealed numerous mast cells which stained metachromatically with giemsa and toluidine blue stain and showed positivity with cd 117. Based on these findings a diagnosis of systemic mastocytosis was made.
Authors and Affiliations
P. Jijiya Bai, Srujana Shyamala, Asok Kumar R.
Keywords
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- EP ID EP420049
- DOI 10.7439/ijbr.v6i11.2514
- Views 102
- Downloads 0
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Systemic Mastocytosis- A Case Report
Mastocytosis is a rare heterogenous disease characterized by the presence of excessive number of mast cells in various organs mainly in skin and bone marrow. .The incidence was 1 in 1,000 to 8,000 patients. It can follow...