Abstract

Rosai–Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a benign, self-limited, idiopathic proliferative histiocytic disorder originally described by Destombes in 1965 and later in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with fever, polyclonal gammopathy and leukocytosis with neutrophilia. The skin is the most common site affected. Extranodal manifestations have been reported in 43% of cases. In the present case report a young male from Asian origin diagnosed to be suffering from RDD is discussed

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